JORDI TAMARIT SUMALLA-rekin lankidetzan egindako argitalpenak (18)
2024
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Calcitriol Treatment Is Safe and Increases Frataxin Levels in Friedreich Ataxia Patients
Movement Disorders
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Mitochondrial impairment, decreased sirtuin activity and protein acetylation in dorsal root ganglia in Friedreich Ataxia models
Cellular and Molecular Life Sciences, Vol. 81, Núm. 1
2022
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Mice harboring the FXN I151F pathological point mutation present decreased frataxin levels, a Friedreich ataxia-like phenotype, and mitochondrial alterations
Cellular and Molecular Life Sciences, Vol. 79, Núm. 2
2021
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Calcitriol increases frataxin levels and restores mitochondrial function in cell models of Friedreich Ataxia
Biochemical Journal, Vol. 478, Núm. 1, pp. 1-20
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Calpain-Inhibitors Protect Frataxin-Deficient Dorsal Root Ganglia Neurons from Loss of Mitochondrial Na+/Ca2+ Exchanger, NCLX, and Apoptosis
Neurochemical Research, Vol. 46, Núm. 1, pp. 108-119
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Mitochondrial iron and calcium homeostasis in Friedreich ataxia
IUBMB Life
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PPAR gamma agonist leriglitazone improves frataxin-loss impairments in cellular and animal models of Friedreich Ataxia
Neurobiology of Disease, Vol. 148
2020
2018
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Frataxin-deficient neurons and mice models of Friedreich ataxia are improved by TAT-MTScs-FXN treatment
Journal of Cellular and Molecular Medicine, Vol. 22, Núm. 2, pp. 834-848
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Iron in friedreich ataxia: A central role in the pathophysiology or an epiphenomenon?
Pharmaceuticals, Vol. 11, Núm. 3
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Mitochondrial calcium signalling and neurodegenerative diseases
Neuronal Signaling, Vol. 2, Núm. 4
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Mitochondrial pore opening and loss of Ca2 + exchanger NCLX levels occur after frataxin depletion
Biochimica et Biophysica Acta - Molecular Basis of Disease, Vol. 1864, Núm. 2, pp. 618-631
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Nitric oxide prevents Aft1 activation and metabolic remodeling in frataxin-deficient yeast
Redox Biology, Vol. 14, pp. 131-141
2017
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Specificity of Protein Carbonylation and Its Relevance in Aging
Protein Carbonylation: Principles, Analysis, and Biological Implications (wiley), pp. 340-383
2016
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Oxidative stress and altered lipid metabolism in Friedreich ataxia
Free Radical Biology and Medicine, Vol. 100, pp. 138-146
2009
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Proteomic and oxidative stress analysis in human brain samples of Huntington disease
Proteómica: revista de la Sociedad Española de Proteómica, Núm. 3, pp. 209-209
2008
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Estrategias proteómicas para el análisis de grupos carbonilo como marcadores de daño oxidativo en proteínas
Proteómica: revista de la Sociedad Española de Proteómica, Núm. 2, pp. 51-58
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Major targets of iron-induced protein oxidative damage in frataxin-deficient yeast magnesium-binding proteins
Proteómica: revista de la Sociedad Española de Proteómica, Núm. 1, pp. 53-54