Publicaciones (75) Publicaciones de JOAQUIN ROS SALVADOR

2024

  1. Calcitriol Treatment Is Safe and Increases Frataxin Levels in Friedreich Ataxia Patients

    Movement Disorders

  2. Mitochondrial impairment, decreased sirtuin activity and protein acetylation in dorsal root ganglia in Friedreich Ataxia models

    Cellular and Molecular Life Sciences, Vol. 81, Núm. 1

2022

  1. Mice harboring the FXN I151F pathological point mutation present decreased frataxin levels, a Friedreich ataxia-like phenotype, and mitochondrial alterations

    Cellular and Molecular Life Sciences, Vol. 79, Núm. 2

2021

  1. Calcitriol increases frataxin levels and restores mitochondrial function in cell models of Friedreich Ataxia

    Biochemical Journal, Vol. 478, Núm. 1, pp. 1-20

  2. Calpain-Inhibitors Protect Frataxin-Deficient Dorsal Root Ganglia Neurons from Loss of Mitochondrial Na+/Ca2+ Exchanger, NCLX, and Apoptosis

    Neurochemical Research, Vol. 46, Núm. 1, pp. 108-119

  3. Mitochondrial iron and calcium homeostasis in Friedreich ataxia

    IUBMB Life

  4. PPAR gamma agonist leriglitazone improves frataxin-loss impairments in cellular and animal models of Friedreich Ataxia

    Neurobiology of Disease, Vol. 148

2020

  1. Frataxin-deficient cardiomyocytes present an altered thiol-redox state which targets actin and pyruvate dehydrogenase

    Redox Biology, Vol. 32

  2. Mitochondrial localization of the yeast forkhead factor hcm1

    International Journal of Molecular Sciences, Vol. 21, Núm. 24, pp. 1-11

  3. Tau inhibits mitochondrial calcium efflux and makes neurons vulnerable to calcium-induced cell death

    Cell Calcium, Vol. 86

2018

  1. Frataxin-deficient neurons and mice models of Friedreich ataxia are improved by TAT-MTScs-FXN treatment

    Journal of Cellular and Molecular Medicine, Vol. 22, Núm. 2, pp. 834-848

  2. Hippocampal neurons require a large pool of glutathione to sustain dendrite integrity and cognitive function

    Redox Biology, Vol. 19, pp. 52-61

  3. Iron in friedreich ataxia: A central role in the pathophysiology or an epiphenomenon?

    Pharmaceuticals, Vol. 11, Núm. 3

  4. Mitochondrial calcium signalling and neurodegenerative diseases

    Neuronal Signaling, Vol. 2, Núm. 4

  5. Mitochondrial pore opening and loss of Ca2 + exchanger NCLX levels occur after frataxin depletion

    Biochimica et Biophysica Acta - Molecular Basis of Disease, Vol. 1864, Núm. 2, pp. 618-631

  6. Nitric oxide prevents Aft1 activation and metabolic remodeling in frataxin-deficient yeast

    Redox Biology, Vol. 14, pp. 131-141

  7. Redox stress in Marfan syndrome: Dissecting the role of the NADPH oxidase NOX4 in aortic aneurysm

    Free Radical Biology and Medicine, Vol. 118, pp. 44-58

2017

  1. Protein Carbonylation: Principles, Analysis, and Biological Implications

    wiley, pp. 1-400

  2. Specificity of Protein Carbonylation and Its Relevance in Aging

    Protein Carbonylation: Principles, Analysis, and Biological Implications (wiley), pp. 340-383

2016

  1. Oxidative stress and altered lipid metabolism in Friedreich ataxia

    Free Radical Biology and Medicine, Vol. 100, pp. 138-146